69.第一型肝醣堆積症 von Gierke’s disease 係因缺乏下列那一種酵素?
(A)debranching enzyme
(B)branching enzyme
(C)glucose-6-phosphatase
(D)phosphorylase

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統計: A(71), B(35), C(448), D(20), E(0) #1727677

詳解 (共 1 筆)

#5715789

Type1 G6P
Type 2 alpha 1, 4 (溶脢體出問題)

Type 3 Debranching
Type 4 Branching 

Type 5 Muscle glycogen phosphorylase 
Type 6 Liver glycogen phosphorylase 

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